Marfan syndrome

From Medicine GPT
Jump to navigation Jump to search

Marfan syndrome (pronounced: /ˈmɑːrfæn/) is a genetic disorder that affects the body's connective tissue. Connective tissue provides strength and flexibility to structures such as the skin, ligaments, and blood vessels. Marfan syndrome is caused by a defect in the gene that encodes the structure of fibrillin and the elastic fibers, a major component of connective tissue. This defect causes an increase in a protein that results in the features of Marfan syndrome.

Etymology

The syndrome is named after Antoine Marfan, the French pediatrician who first described the condition in 1896 after noticing striking features in a five-year-old girl. The term "syndrome" is derived from the Greek "σύνδρομον", meaning "concurrence".

Symptoms

Marfan syndrome affects different people in different ways. Some people experience only mild symptoms, while others experience severe and life-threatening complications. Symptoms can include:

  • Tall stature
  • Long arms and legs
  • Heart and blood vessel problems
  • Eye problems
  • Skeletal problems

Diagnosis

Marfan syndrome is diagnosed using a variety of methods, including a physical examination, family history, and genetic testing. The Ghent criteria, an internationally recognized tool, is often used to aid in the diagnosis.

Treatment

There is no cure for Marfan syndrome. However, treatment can help to manage symptoms and reduce the risk of complications. Treatment options can include medication, surgery, and lifestyle changes.

Related Terms

See Also

External links

Esculaap.svg

This MedicineGPT article is a stub. You can help make it a full article.


Languages: - East Asian 中文, 日本, 한국어, South Asian हिन्दी, Urdu, বাংলা, తెలుగు, தமிழ், ಕನ್ನಡ,
Southeast Asian Indonesian, Vietnamese, Thai, မြန်မာဘာသာ, European español, Deutsch, français, русский, português do Brasil, Italian, polski