Congenital self-healing reticulohistiocytosis
Congenital Self-Healing Reticulohistiocytosis (kənˈjenɪtəl sɛlfˈhiːlɪŋ ˌrɛtɪkjʊloʊˌhɪstɪoʊsaɪˈtoʊsɪs) is a rare, benign histiocytic disorder that primarily affects newborns. The term is derived from the Latin congenitus meaning "born with", and the Greek histio and kytos meaning "tissue cell", and osis meaning "condition".
Overview
Congenital Self-Healing Reticulohistiocytosis, also known as Hashimoto-Pritzker disease, is characterized by the presence of skin lesions at birth or shortly thereafter. These lesions typically resolve spontaneously within several months. The disorder is considered a variant of Langerhans cell histiocytosis (LCH), but unlike other forms of LCH, it is not associated with long-term complications or recurrence.
Symptoms
The primary symptom of Congenital Self-Healing Reticulohistiocytosis is the presence of skin lesions. These lesions are typically red or purple in color, and may be found anywhere on the body. They are often described as firm, dome-shaped nodules.
Diagnosis
Diagnosis of Congenital Self-Healing Reticulohistiocytosis is typically made based on the characteristic appearance of the skin lesions and their spontaneous resolution. Biopsy of the lesions may be performed to confirm the diagnosis.
Treatment
As the name suggests, Congenital Self-Healing Reticulohistiocytosis typically resolves on its own without treatment. However, in some cases, treatment may be necessary to manage symptoms. This may include topical or systemic corticosteroids.
See Also
External links
- Medical encyclopedia article on Congenital self-healing reticulohistiocytosis
- Wikipedia's article - Congenital self-healing reticulohistiocytosis
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